Adult Kasabach-Merritt Syndrome: A Case Report and Review of Literature

Msheik Aliand Bitar Nizar

Department of Internal Medicine, Lebanese University, Lebanon

^*Correspondance to: Msheik Ali 

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Abstract:

The most common benign liver tumors are cavernous Hemangioma. They can reach enormous sizes and cause varied complications. Kasabach-Merritt syndrome is a constellation of a hemangioma inclusive of endothelial abnormalities, which lead to a consumptive coagulopathy and subsequent thrombocytopenia. Although rare, serious complications are present yielding a mortality rate of 10% to 37%. 80% of cases occur in the first year of life with 0.3% of infants with hemangiomas affected. The treatment aims to control the coagulopathy and thrombocytopenia as well as eradicate the hemangioma. Different treatment approaches are present inclusive of surgical and non-surgical techniques of which systemic corticosteroids, irradiation and immune-suppressors are an option. Surgery is limited to cases of symptomatic and complicated presentations. Although not simple, enucleation is curative usually. Here, we present a 53-year-old man with giant hemangiomas causing KMS.

Keywords:

Hemangiomas; Liver; Kasabach-Merritt Syndrome (KMS)

Cite the Article:

Ali M, Nizar B. Adult Kasabach-Merritt Syndrome: A Case Report and Review of Literature. Clin Case Rep Int. 2022; 6: 1330.